I-Arthrogrypose

I-Arthrogryposis yisifo sokuzalwa esibangela ukuqina kwamalunga. Ngakho-ke ububanzi bokunyakaza bunomkhawulo. Izinkontileka ezihlangene ezihambisana nalesi sifo zikhula esibelethweni futhi izimpawu zikhona kusukela ekuzalweni.

Wonke amalunga angathinteka noma amanye kuphela: izitho, ithorax, umgogodla noma i-temporomaxillary (imihlathi).

Ukuxilongwa kwangaphambi kokubeletha kunzima. Kungenziwa lapho umama ezwa ukuncipha kokunyakaza kwe-fetus. Ukuxilongwa kwenziwa ekuzalweni ngemva kokuhlolwa komtholampilo kanye nama-x-ray. 

Izimbangela ze-arthrogryposis okwamanje azikaziwa.

I-Arthrogryposis, kuyini?

I-Arthrogryposis yisifo sokuzalwa esibangela ukuqina kwamalunga. Ngakho-ke ububanzi bokunyakaza bunomkhawulo. Izinkontileka ezihlangene ezihambisana nalesi sifo zikhula esibelethweni futhi izimpawu zikhona kusukela ekuzalweni.

Wonke amalunga angathinteka noma amanye kuphela: izitho, ithorax, umgogodla noma i-temporomaxillary (imihlathi).

Ukuxilongwa kwangaphambi kokubeletha kunzima. Kungenziwa lapho umama ezwa ukuncipha kokunyakaza kwe-fetus. Ukuxilongwa kwenziwa ekuzalweni ngemva kokuhlolwa komtholampilo kanye nama-x-ray. 

Izimbangela ze-arthrogryposis okwamanje azikaziwa.

Izimpawu ze-arthrogryposis

Singakwazi ukuhlukanisa izinhlobo eziningana ze-arthrogryposis:

I-Arthrogryposis Multiple Congenital (MCA)

Kuyifomu okuvame ukuhlangatshezwana nalo, ngokohlelo lokuzala okuthathu kwabayi-10. 

Kuthinta zonke izitho ezine kuma-45% ezimweni, kuphela izitho ezingezansi kuma-45% ezimweni kanye nezitho ezingaphezulu kuphela ku-10% wezimo.

Ezimweni eziningi amalunga athinteka ngokulinganayo.

Cishe i-10% yeziguli inokukhubazeka kwesisu ngenxa yokwakheka kwemisipha okungavamile.

Amanye ama-arthrogryposes

Izimo eziningi ze-fetus, i-genetic syndromes noma i-malformative syndrome inesibopho sokuqina kwamalunga. Ezikhathini eziningi kukhona ukungahambi kahle kobuchopho, umgogodla kanye ne-viscera. Ezinye ziholela ekulahlekelweni okukhulu kokuzimela futhi zisongela ukuphila. 

  • I-Hecht syndrome noma i-trismus-pseudo camptodactyly: ihlobanisa ubunzima bokuvula umlomo, ukukhubazeka ekwandiseni iminwe nesihlakala nezinyawo ze-equine noma i-convex varus club. 
  • I-Freeman-Shedon noma i-cranio-carpo-tarsal syndrome, eyaziwa nangokuthi ingane eshaya ikhwela: sibona ubuso obuthile obunomlomo omncane, ikhala elincane, amaphiko angathuthukisiwe ekhala kanye ne-epicanthus (ukugoqa kwesikhumba okumise okwe ingxenye yenyanga ekhoneni elingaphakathi leso).
  • I-Moebius syndrome: ihlanganisa i-clubfoot, ukukhubazeka kweminwe, nokukhubazeka kobuso bamazwe amabili.

Ukwelashwa kwe-arthrogryposis

Ukwelashwa akuhlosile ukwelapha lesi sifo kodwa ukunikeza umsebenzi ohlangene ongcono kakhulu. Zincike ohlotsheni kanye nezinga le-arthrogryposis. Kuye ngecala, kungase kunconywe:

  • Ukuvuselelwa okusebenzayo ukulungisa ukukhubazeka. Lapho ukuvuselelwa kusenesikhathi, ukunyakaza okuncane kuzonqunyelwa.
  • Physiotherapy.
  • Ukuhlinzwa kokuhlinzwa: ikakhulukazi esimweni sonyawo lweklabhu, inqulu ehlakazekile, ukulungiswa kwe-axis yesitho, ukunwetshwa kwemisipha noma ukudluliselwa kwemisipha.
  • Ukusetshenziswa kwe-orthopedic corset esimweni sokukhubazeka komgogodla.

Umkhuba wezemidlalo awunqatshelwe futhi kufanele ukhethwe ngokwamandla esiguli.

Ukuvela kwe-arthrogryposis

Ukuqina kwamalunga akubi kubi ngemva kokuzalwa. Kodwa-ke, ngesikhathi sokukhula, ukungasebenzisi izitho noma ukuzuza kwesisindo esikhulu kungaholela ekukhubazekeni okuphawulekayo kwamathambo.

Amandla emisipha athuthukiswa kancane kakhulu. Ngakho-ke kungenzeka ukuthi akusanele ezithweni ezithile esigulini esikhulile.

Le syndrome ingakhubaza ikakhulukazi ezimweni ezimbili:

  • Lapho ukuhlasela kwemilenze engezansi edinga idivayisi ukuze ime iqonde. Lokhu kudinga ukuthi umuntu akwazi ukuyibeka yedwa ukuze akwazi ukuzimela futhi ngenxa yalokho abe nokusetshenziswa cishe okuvamile kwezitho zakhe zangaphezulu. Lokhu kusetshenziswa kufanele futhi kuphelele uma, ukuhambahamba, usizo lwezinduku luyadingeka.
  • Lapho ukuphumelela kwezitho ezine kudinga ukusetshenziswa kwesihlalo esinamasondo sikagesi kanye nokusetshenziswa komuntu wesithathu.

shiya impendulo