Yini i-hemochromatosis

Yini i-hemochromatosis

I-Hemochromatosis (ebuye ibizwe ngokuthi i-genetic hemochromatosis noma i-hemochromatosis yofuzo) isifo esiwufuzo futhi esitholakala njengefa ukumuncwa kwe-iron ngokweqile ngethumbu kanye nalo ukunqwabelana emzimbeni.

Izinkinga ze-hemochromatosis

I-Hemochromatosis yisifo sofuzo esixhumene ne-a ukuguqulwa kohlobo olulodwa noma eziningi. Lezi zinguquko zibhekwa ezifundeni ezihlukene zomhlaba futhi ngayinye ihambisana nokubonakaliswa kwesifo esibi kakhulu.

THEi-hemochromatosis i-HFE yofuzo (ebizwa nangokuthi uhlobo lwe-hemochromatosis) uhlobo oluvame kakhulu lwesifo. Ixhunywe ekuguqukeni kofuzo lwe-HFE olutholakala ku-chromosome 6.

Imvamisa yalesi sifo

I-Hemochromatosis ingenye yezifo ezivame kakhulu zofuzo.

Cishe umuntu oyedwa kwabangu-1 unesici sofuzo esenza ukuba lesi sifo siqale1. Kodwa okufanele kuqondwe manje ukuthi lesi sifo singaba nokubonakaliswa komtholampilo kokuqina okuguquguqukayo ukuze izinhlobo ezinzima ze-hemochromatosis zihlale ziyivelakancane.

Abantu abahlaselwe yilesi sifo

The amadoda bavame ukuthinteka kakhulu kunabesifazane (amadoda ama-3 kowesifazane oyedwa).

Izimpawu zivela kaningi Eminyakeni engama-40 ngemuva kepha ingaqala phakathi kweminyaka engu-5 nengama-30 ubudala (i-juvenile hemochromatosis).

Lesi sifo sivame ukubonwa ezindaweni ezithile zomhlaba, isibonelo e-United States noma enyakatho yeYurophu. Ayitholakali emazweni aseNingizimu-mpumalanga ye-Asia noma kubantu abamnyama.

E-France, ezinye izifunda (i-Brittany) zithinteka kakhulu.

shiya impendulo