Okuqukethwe
Yini i-hemochromatosis
I-Hemochromatosis (ebuye ibizwe ngokuthi i-genetic hemochromatosis noma i-hemochromatosis yofuzo) isifo esiwufuzo futhi esitholakala njengefa ukumuncwa kwe-iron ngokweqile ngethumbu kanye nalo ukunqwabelana emzimbeni.
Izinkinga ze-hemochromatosis
I-Hemochromatosis yisifo sofuzo esixhumene ne-a ukuguqulwa kohlobo olulodwa noma eziningi. Lezi zinguquko zibhekwa ezifundeni ezihlukene zomhlaba futhi ngayinye ihambisana nokubonakaliswa kwesifo esibi kakhulu.
THEi-hemochromatosis i-HFE yofuzo (ebizwa nangokuthi uhlobo lwe-hemochromatosis) uhlobo oluvame kakhulu lwesifo. Ixhunywe ekuguqukeni kofuzo lwe-HFE olutholakala ku-chromosome 6.
Imvamisa yalesi sifo
I-Hemochromatosis ingenye yezifo ezivame kakhulu zofuzo.
Cishe umuntu oyedwa kwabangu-1 unesici sofuzo esenza ukuba lesi sifo siqale1. Kodwa okufanele kuqondwe manje ukuthi lesi sifo singaba nokubonakaliswa komtholampilo kokuqina okuguquguqukayo ukuze izinhlobo ezinzima ze-hemochromatosis zihlale ziyivelakancane.
Abantu abahlaselwe yilesi sifo
The amadoda bavame ukuthinteka kakhulu kunabesifazane (amadoda ama-3 kowesifazane oyedwa).
Izimpawu zivela kaningi Eminyakeni engama-40 ngemuva kepha ingaqala phakathi kweminyaka engu-5 nengama-30 ubudala (i-juvenile hemochromatosis).
Lesi sifo sivame ukubonwa ezindaweni ezithile zomhlaba, isibonelo e-United States noma enyakatho yeYurophu. Ayitholakali emazweni aseNingizimu-mpumalanga ye-Asia noma kubantu abamnyama.
E-France, ezinye izifunda (i-Brittany) zithinteka kakhulu.