Ukwelashwa, ukuphathwa, ukuvimbela i-hemochromatosis

Ukwelashwa, ukuphathwa, ukuvimbela i-hemochromatosis

Ukwelashwa kwe-hemochromatosis kusekelwe ukuphuma kwegazi (ebizwa nangokuthi i-phlebotomies). Bahlose ukwehlisa izinga le-iron egazini futhi banciphise i-iron deposits emzimbeni ngaphandle kokubangela ukuntuleka kwe-iron anemia.

Inqubo iyafana naleyo eyenziwa lapho kunikelwa igazi. Kunconywa ukuphuza amanzi ngemva kokuphuma kwegazi.

Kuyindlela yokwelapha elula, engabizi futhi ephumelelayo, ngokuvamile eyenziwa phakathi kuka-4 no-6 izikhathi ngonyaka, ngaphandle komthelela empilweni yesiguli, ikakhulukazi njengoba ukopha kungenziwa ekhaya.

Udokotela uchaza inani legazi okufanele lithathwe kuvela njalo esigulini kucatshangelwa iminyaka yaso, isisindo nobude baso. Ekuqaleni, ukuchithwa kwegazi kwamasonto onke kuyadingeka futhi kugcinwa inqobo nje uma ukugcwala kwensimbi kubonakala. Lapho izinga le-ferritin egazini liwela ngaphansi kwe-50 μg / L, zenziwa njalo ngenyanga noma ngekota njengoba kungenzeka ukugcina izinga le-ferritin egazini elingaphansi kwe-50 μg / L. Zizogcinwa impilo yonke.

Lokhu kwelashwa akuselapha isifo.

Kwabesifazane abakhulelwe, ukopha akwenziwa ngesikhathi sokukhulelwa. Ukufakwa kwe-ayina akudingekile.

Ezinye izinkinga zesifo (i-cirrhosis, ukwehluleka kwenhliziyo noma isifo sikashukela) ziyisihloko sokwelashwa okuqondile.


Qaphela ukuthi akukho ukudla okungashintsha ukwelashwa ngokopha. Isiguli sinconywa ukuba silandele ukudla okuvamile futhi sinciphise ukuphuza utshwala.

 

Izinzuzo zokwelashwa

Ngokwelashwa, ukukhathala okuvame ukubonakala ezigulini ezine-hemochromatosis kuncipha. Ikakhulukazi, lapho ukwelashwa kuqalwa kusenesikhathi, kuyasiza ukugwema izinkinga ezingathi sína zesifo (ukulimala kwenhliziyo, isibindi namanyikwe) ngaleyo ndlela andise isikhathi sokuphila kweziguli.

Alukho ushintsho emikhubeni yeziguli okufanele lucatshangelwe ku-hemochromatosis ngaphandle kwemithetho yenhlanzeko yokuphila ehlanganisa ukudla okuvamile kanye nokunciphisa uphuzo oludakayo uma ukweqisa bekwenziwa ngaphambilini.

Iziguli zigadwa eminyangweni ye-hepato-gastroenterology. Kubantu abasengozini, ukubonisana ngofuzo kukhonjiswe ngokuphelele ukuze kutholwe lesi sifo kusenesikhathi futhi kuthathwe izinyathelo zokwelapha ezidingekayo.

E-France, izinhlobo ezithuthukisiwe ze-hemochromatosis zingenye yezimo zesikhathi eside ezingama-30 (ALD 30).

shiya impendulo