UClaude Bernard-Horner syndrome

UClaude Bernard-Horner syndrome

Umphumela we-ocular sympathetic nerve paralysis, i-Claude Bernard-Horner syndrome izibonakalisa nge-ptosis yejwabu leso eliphezulu, ukuncipha komfundi kanye nokungabi bikho kokujuluka ohlangothini oluthintekile lobuso. Kungaba uphawu lwe-pathology eyisisekelo.

Claude Bernard-Horner syndrome, kuyini?

Incazelo

I-Claude Bernard-Horner syndrome iyisifo sezinzwa esithinta ingxenye yobuso, futhi ikakhulukazi iso.

Izimbangela

I-Claude Bernard-Horner syndrome ingenzeka ngokuzenzakalelayo (ifomu eliyinhloko), noma ibe umphumela wesilonda semicu yesimiso sezinzwa esinozwela esingavaleli umzila. Ezinye zazo zehla ngomgogodla, ziphume ziqhamuke emthonjeni bese zikhuphuka zihambisana nentamo esweni. Futhi, ukulimala noma ukucindezela endleleni yale micu yezinzwa kungaholela ku-Claude Bernard-Horner syndrome. Lesi silonda singaba phakathi (ebuchosheni) noma se-peripheral (esiqwini esizwelayo somlomo wesibeletho). Leyo :

  • ukuhlukaniswa kwe-carotid;
  • ingozi ye-cerebral vascular;
  • i-lymphadenopathy yomlomo wesibeletho (ama-lymph nodes entanyeni);
  • isimila, ikakhulukazi sephaphu, esicindezela inzwa enozwela;
  • ukuhlinzwa komgogodla wesibeletho (okungavamile).

Qaphela ukuthi kukhona futhi izinhlobo zokuzalwa ze-Claude Bernard-Horner syndrome.

kwesifo

Ukuqinisekiswa kokuxilongwa kwe-Claude-Bernard-Horner syndrome kusekelwe ekufakweni kwamaconsi esweni e-cocaine (4 noma 10%) noma i-apraclonidine (0,5 noma 1%). I-Cocaine iyi-sympathomometic engaqondile: ibangela ukuvuleka komfundi. Ku-Claude Bernard-Horner syndrome, umfundi othintekile ngeke anwebe kanye nomunye umfundi. I-Apraclonidine, ngakolunye uhlangothi, inesenzo kuma-receptors athile wokuhlanjululwa komfundi. Uma kwenzeka i-Claude Bernard-Horner syndrome, izobangela ukuvuleka komfundi.

Uma ukuxilongwa kwe-Claude Bernard-Horner syndrome kuqinisekiswa, emahoreni angu-48 kamuva ukuhlolwa kwe-ophthalmic kusetshenziswa amaconsi e-hydroxyamphetamine kungenziwa ukuze kutholakale isilonda, ngaphambili noma i-postganglionic.

I-Claude-Bernard-Horner syndrome triad, ubuhlungu obuhlangene ekhanda, ebusweni nasentanyeni futhi, amahora ambalwa noma izinsuku ezimbalwa kamuva, i-ischemia ye-ipspheric noma ipsilateral retinal iphakamisa i-carotid dissection. I-doppler ultrasound yombala womlomo wesibeletho bese kuba ukuhlolwa komugqa wokuqala.

Kuye ngesimo somtholampilo, i-MRI yobuchopho, intambo yomgogodla, i-thorax noma intamo ingase ibekwe ukuze kutholakale isilonda, futhi kutholwe i-pathology engenzeka ekuqaleni kwe-syndrome.

Abantu abathintekayo

I-Claude Bernard-Horner syndrome ingenzeka kunoma iyiphi iminyaka.

Izimpawu ze-Claude Bernard-Horner syndrome

Izimpawu ze-Claude Bernard-Horner syndrome zivela ohlangothini lobuso lapho izintambo zemizwa zilimele khona. Bahlanganisa:

  • i-ptosis yejwabu leso eliphezulu: ijwabu leso elingenhla liyawa ngenxa yokukhubazeka kwemisipha ebushelelezi yemisipha ehambisana ne-levator yejwabu leso eliphezulu;
  • ukwakhiwa komfundi (miosis), ngenxa yokukhubazeka kwemisipha ye-dilator yomfundi. Umfundi uyancishiswa, kodwa ngokuvamile awanamthelela embonweni, noma akuvamile ukuthi abone ebusuku kwezinye iziguli;
  • ukujuluka kwehle ohlangothini oluthintekile lobuso, ngezinye izikhathi ngeziqephu zobubomvu.

Ukwelashwa kwe-Claude Bernard-Horner syndrome

Ukwelapha i-Claude Bernard-Horner syndrome, kungumbuzo wokwelapha imbangela emsuka we-Claude Bernard-Horner syndrome.

shiya impendulo