Ziyini izimpawu ze-hemochromatosis?
Izimpawu zixhunyaniswa nokufakwa kwe-iron ezithweni ezahlukahlukene njengesikhumba, inhliziyo, izindlala ze-endocrine nesibindi.
Ukuvela kwezimpawu zesifo
– Phakathi kweminyaka engu-0 no-20, insimbi inqwabelana kancane kancane emzimbeni ngaphandle kokubangela izimpawu.
– Phakathi kweminyaka engama-20 nengama-40, kuvela ukugcwala kwensimbi okungakaziniki izimpawu.
Maphakathi neminyaka eyishumi yesine emadodeni (futhi kamuva kwabesifazane), izimpawu zokuqala zomtholampilo zalesi sifo ziyavela: ukukhathala Unomphela ubuhlungu bamalunga (amalunga amancane eminwe, izihlakala noma ezinqulwini), ukunsundu kwesikhumba (i-melanoderma), ukubukeka “okumpunga, okwensimbi” kwesikhumba ebusweni, amalunga amakhulu nezitho zangasese, i-atrophy yesikhumba (isikhumba siba mncane), ukubukeka kwescaly noma isikali senhlanzi (yilokhu okubizwa nge-ichthyosis) esikhumbeni kanye nokuncipha kwesikhumba. izinwele kanye nezinwele ze-pubic
- Uma isifo singakatholakali, kuvela izinkinga ezithinta isifo isibindi, inhliziyo futhi izindlala ze-endocrine.
Ukulimala kwesibindi : ekuhlolweni komtholampilo, udokotela angase abone ukwanda kobukhulu besibindi, obhekene nobuhlungu besisu. I-Cirrhosis kanye nokuqala komdlavuza wesibindi yizinkinga ezimbi kakhulu zalesi sifo.
Ukuphazamiseka kwe-endocrine : inkambo yalesi sifo ingabonakala ngokuvela kwesifo sikashukela (ukulimala kwe-pancreas) kanye nokungabi namandla emadodeni (ukulimala kwamasende).
Ukulimala kwenhliziyo : Idiphozi yensimbi enhliziyweni inesibopho sokwanda komthamo wayo kanye nezimpawu zokwehluleka kwenhliziyo.
Ngakho-ke, uma lesi sifo sitholakala kuphela ekupheleni kwesikhathi (izimo ezisele zingavamile namuhla), kungenzeka ukuthi kubhekwe ukuhlangana kokuhluleka kwenhliziyo, isifo sikashukela kanye ne-cirrhosis yesibindi. kanye nokushintsha kombala wesikhumba okunsundu.
Uma lesi sifo sitholwa ngaphambi kwesikhathi (ngaphambi kweminyaka engama-40), kuba ngcono ukusabela ekwelashweni kanye nokubikezelwa okuhle kwesifo.. Ngakolunye uhlangothi, lapho izinkinga ezichazwe ngenhla zivela, ziyahlehla kancane lapho zelashwa. Uma isiguli selashwa ngaphambi kokuqala kwe-cirrhosis, isikhathi sokuphila saso siyefana nesabo bonke abantu.